Basal Cell Carcinoma in Type 2 Segmental Darier's Disease

Robertson, Lynne; Sauder, Maxwell B.

Basal Cell Carcinoma in Type 2 Segmental Darier's Disease

dc.contributor.author	Robertson, Lynne
dc.contributor.author	Sauder, Maxwell B.
dc.date.accessioned	2018-09-27T11:55:14Z
dc.date.available	2018-09-27T11:55:14Z
dc.date.issued	2011-07-31
dc.date.updated	2018-09-27T11:55:14Z
dc.description.abstract	Background. Darier's disease (DD), also known as Keratosis Follicularis or Darier-White disease, is a rare disorder of keratinization. DD can present as a generalized autosomal dominant condition as well as a localized or segmental postzygotic condition (Vázquez et al., 2002). Clinical features of DD include greasy, warty papules and plaques on seborrheic areas, dystrophic nails, palmo-plantar pits, and papules on the dorsum of the hands and feet. Objective. We report a case of basal cell carcinoma developing in a patient with type 2 segmental DD. Conclusion. According to the current literature, Type 2 segmental disease is a rare presentation of Darier's disease with only 8 previous cases reported to date. In addition, nonmelanoma skin cancer (NMSC) arising from DD is rarely reported; however, there may be an association between DD and risk of carcinogenesis.
dc.description.version	Peer Reviewed
dc.identifier.citation	Lynne Robertson and Maxwell B. Sauder, “Basal Cell Carcinoma in Type 2 Segmental Darier's Disease,” Journal of Skin Cancer, vol. 2012, Article ID 839561, 4 pages, 2012. doi:10.1155/2012/839561
dc.identifier.doi	https://doi.org/10.1155/2012/839561
dc.identifier.uri	http://hdl.handle.net/1880/108387
dc.language.rfc3066	en
dc.rights.holder	Copyright © 2012 Lynne Robertson and Maxwell B. Sauder. This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
dc.title	Basal Cell Carcinoma in Type 2 Segmental Darier's Disease
dc.type	Journal Article